Fig. 5 Pericentral retinitis pigmentosa. Pigment epithelial atrophy and associated pigmentations surround an intact central macula. As the disease in this patient is fairly advanced, the retinal vessels show moderate attenuation. (Courtesy of Dr. Roland Sabutes: Fenestrated sheen macular dystrophy: A new autosomal dominant maculopathy. Arch. Ophthalmol. 97:1293, 1979. Copyright © 1979 American Medical Association.)