Fig. 2. Golden tapetal reflexes. There are three diseases in which there is an unusual golden reflex to the fundus: X-linked recessive RP in the carrier female, Oguchi's disease, and cone dystrophy. In all these diseases the angiogram is essentially normal, suggesting that this reflex is probably not related to pigment abnormalities. A, B. Carrier female of XLR retinitis pigmentosa. A golden scintillating reflex radiates from the macula. C, D. Oguchi's disease. A diffuse yellow metallic sheen is seen in the posterior pole (a pigmented chorioretinal lesion is an incidental finding). E, F. Progressive cone dystrophy. The typical bull's eye maculopathy is associated with a golden orange reflex.