Fig. 4. A. Choroideremia in a male patient. There is loss of the retinal pigment epithelium and prominence of the choroidal pattern in the periphery. There is sparing of the macular region. B. Portions of the retinal pigment epithelium under the fovea still are intact in the late stages of choroideremia. (A and B courtesy of J. M. D. Gass, M.D.)