Fig. 6 Pericentral retinitis pigmentosa. Fellow eye of patient photographed in Fig. 5 demonstrates the large annular zone of pigment epithelial atrophy and pigmentations surrounding an intact central macula. Note the unaffected retina peripheral to this annular zone of involvement. (Courtesy of Dr. Roland Sabutes: Fenestrated sheen macular dystrophy: A new autosomal dominant maculopathy. Arch. Ophthalmol. 97:1293, 1979. Copyright © 1979 American Medical Association.)